Q89.81Billable
Kabuki syndrome
- Chapter
- 17. Congenital malformations, deformations and chromosomal abnormalities
- Category
- Q89
- Effective date
- October 1, 2026
Related codes in category Q89
Q89Other congenital malformations, not elsewhere classifiedQ89.0Congenital absence and malformations of spleenQ89.01Asplenia (congenital)YesQ89.09Congenital malformations of spleenYesQ89.1Congenital malformations of adrenal glandYesQ89.2Congenital malformations of other endocrine glandsYesQ89.3Situs inversusYesQ89.4Conjoined twinsYesQ89.7Multiple congenital malformations, not elsewhere classifiedYesQ89.8Other specified congenital malformationsQ89.89Other specified congenital malformationsYesQ89.9Congenital malformation, unspecifiedYes
Frequently asked questions
What is ICD-10 code Q89.81?
Q89.81 is an ICD-10-CM diagnosis code for Kabuki syndrome.
Is Q89.81 a billable code?
Yes. Q89.81 is billable and specific enough to be used on a claim.
What ICD-10-CM chapter is Q89.81 in?
Q89.81 falls under Chapter 17: Congenital malformations, deformations and chromosomal abnormalities.
When did Q89.81 become effective?
Q89.81 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to Q89.81?
Q89.81 belongs to category Q89, which includes 12 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.