N01Header code — not billable
Rapidly progressive nephritic syndrome
- Chapter
- 14. Diseases of the genitourinary system
- Category
- N01
- Effective date
- October 1, 2026
Related codes in category N01
N01.0Rapidly progr nephritic syndrome w minor glomerular abnltYesN01.1Rapidly progr neph synd w focal and seg glomerular lesionsYesN01.2Rapidly progr neph syndrome w diffuse membranous glomrlnephYesN01.3Rapidly progr neph synd w diffus mesangial prolif glomrlnephYesN01.4Rapid progr neph synd w diffus endocaplry prolif glomrlnephYesN01.5Rapidly progr neph syndrome w diffuse mesangiocap glomrlnephYesN01.6Rapidly progr nephritic syndrome w dense deposit diseaseYesN01.7Rapidly progr neph syndrome w diffuse crescentic glomrlnephYesN01.8Rapidly progr nephritic syndrome w oth morphologic changesYesN01.9Rapidly progr nephritic syndrome w unsp morphologic changesYesN01.ARapidly progressive nephritic syndrome with C3 glomrlnephYes
Frequently asked questions
What is ICD-10 code N01?
N01 is an ICD-10-CM diagnosis code for Rapidly progressive nephritic syndrome.
Is N01 a billable code?
No. N01 is a category/header code, not billable on its own — use one of its more specific child codes instead.
What ICD-10-CM chapter is N01 in?
N01 falls under Chapter 14: Diseases of the genitourinary system.
When did N01 become effective?
N01 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to N01?
N01 belongs to category N01, which includes 11 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.