E88.01Billable
Alpha-1-antitrypsin deficiency
- Chapter
- 4. Endocrine, nutritional and metabolic diseases
- Category
- E88
- Effective date
- October 1, 2026
Related codes in category E88
E88Other and unspecified metabolic disordersE88.0Disorders of plasma-protein metabolism, NECE88.02Plasminogen deficiencyYesE88.09Oth disorders of plasma-protein metabolism, NECYesE88.1Lipodystrophy, not elsewhere classifiedE88.10Lipodystrophy, unspecifiedYesE88.11Partial lipodystrophyYesE88.12Generalized lipodystrophyYesE88.13Localized lipodystrophyYesE88.14HIV-associated lipodystrophyYesE88.19Other lipodystrophy, not elsewhere classifiedYesE88.2Lipomatosis, not elsewhere classifiedYes
Frequently asked questions
What is ICD-10 code E88.01?
E88.01 is an ICD-10-CM diagnosis code for Alpha-1-antitrypsin deficiency.
Is E88.01 a billable code?
Yes. E88.01 is billable and specific enough to be used on a claim.
What ICD-10-CM chapter is E88.01 in?
E88.01 falls under Chapter 4: Endocrine, nutritional and metabolic diseases.
When did E88.01 become effective?
E88.01 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to E88.01?
E88.01 belongs to category E88, which includes 12 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.