E76.0Header code — not billable
Mucopolysaccharidosis, type I
- Chapter
- 4. Endocrine, nutritional and metabolic diseases
- Category
- E76
- Effective date
- October 1, 2026
Related codes in category E76
E76Disorders of glycosaminoglycan metabolismE76.01Hurler's syndromeYesE76.02Hurler-Scheie syndromeYesE76.03Scheie's syndromeYesE76.1Mucopolysaccharidosis, type IIYesE76.2Other mucopolysaccharidosesE76.21Morquio mucopolysaccharidosesE76.210Morquio A mucopolysaccharidosesYesE76.211Morquio B mucopolysaccharidosesYesE76.219Morquio mucopolysaccharidoses, unspecifiedYesE76.22Sanfilippo mucopolysaccharidosesYesE76.29Other mucopolysaccharidosesYes
Frequently asked questions
What is ICD-10 code E76.0?
E76.0 is an ICD-10-CM diagnosis code for Mucopolysaccharidosis, type I.
Is E76.0 a billable code?
No. E76.0 is a category/header code, not billable on its own — use one of its more specific child codes instead.
What ICD-10-CM chapter is E76.0 in?
E76.0 falls under Chapter 4: Endocrine, nutritional and metabolic diseases.
When did E76.0 become effective?
E76.0 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to E76.0?
E76.0 belongs to category E76, which includes 12 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.