E74.00Billable
Glycogen storage disease, unspecified
- Chapter
- 4. Endocrine, nutritional and metabolic diseases
- Category
- E74
- Effective date
- October 1, 2026
Related codes in category E74
E74Other disorders of carbohydrate metabolismE74.0Glycogen storage diseaseE74.01von Gierke diseaseYesE74.02Pompe diseaseYesE74.03Cori diseaseYesE74.04McArdle diseaseYesE74.05Lysosome-associated membrane protein 2 [LAMP2] deficiencyYesE74.09Other glycogen storage diseaseYesE74.1Disorders of fructose metabolismE74.10Disorder of fructose metabolism, unspecifiedYesE74.11Essential fructosuriaYesE74.12Hereditary fructose intoleranceYes
Frequently asked questions
What is ICD-10 code E74.00?
E74.00 is an ICD-10-CM diagnosis code for Glycogen storage disease, unspecified.
Is E74.00 a billable code?
Yes. E74.00 is billable and specific enough to be used on a claim.
What ICD-10-CM chapter is E74.00 in?
E74.00 falls under Chapter 4: Endocrine, nutritional and metabolic diseases.
When did E74.00 become effective?
E74.00 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to E74.00?
E74.00 belongs to category E74, which includes 12 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.