E71Header code — not billable
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Short description: Disord of branched-chain amino-acid metab & fatty-acid metab
- Chapter
- 4. Endocrine, nutritional and metabolic diseases
- Category
- E71
- Effective date
- October 1, 2026
Related codes in category E71
E71.0Maple-syrup-urine diseaseYesE71.1Other disorders of branched-chain amino-acid metabolismE71.11Branched-chain organic aciduriasE71.110Isovaleric acidemiaYesE71.1113-methylglutaconic aciduriaYesE71.118Other branched-chain organic aciduriasYesE71.12Disorders of propionate metabolismE71.120Methylmalonic acidemiaYesE71.121Propionic acidemiaYesE71.128Other disorders of propionate metabolismYesE71.19Other disorders of branched-chain amino-acid metabolismYesE71.2Disorder of branched-chain amino-acid metabolism, unspYes
Frequently asked questions
What is ICD-10 code E71?
E71 is an ICD-10-CM diagnosis code for Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.
Is E71 a billable code?
No. E71 is a category/header code, not billable on its own — use one of its more specific child codes instead.
What ICD-10-CM chapter is E71 in?
E71 falls under Chapter 4: Endocrine, nutritional and metabolic diseases.
When did E71 become effective?
E71 has been effective since October 1, 2026, per the CMS/CDC ICD-10-CM annual release.
What other codes are related to E71?
E71 belongs to category E71, which includes 12 other codes — see the related codes list on this page.
ICD-10-CM data maintained by CDC/CMS (public domain). Always verify codes with authoritative sources before making coding or billing decisions.